Cluster 1 | Cluster 2 | Cluster 3 | Cluster 4 | Cluster 5 | ||||||
---|---|---|---|---|---|---|---|---|---|---|
n = 33 | n = 18 | n = 4 | n = 8 | n = 16 | ||||||
n | % | n | % | n | % | n | % | n | % | |
Type of PHID | ||||||||||
CVID | 23 | (70) | 8 | (44) | 3 | (75) | 8 | (100) | 13 | (82) |
IgG subclass deficiency | 10 | (30) | 10 | (56) | 0 | (0) | 0 | (0) | 1 | (6) |
Good’s syndrome | 0 | (0) | 0 | (0) | 1 | (25) | 0 | (0) | 2 | (12) |
PHID complications (at least one of the following) | 5 | (15) | 6 | (33) | 3 | (75) | 7 | (88) | 10 | (63) |
Lymphoid hyperplasia | 2 | (6) | 5 | (28) | 1 | (25) | 3 | (38) | 5 | (31) |
Splenomegaly | 1 | (3) | 2 | (11) | 1 | (25) | 7 | (88) | 3 | (19) |
Autoimmune manifestations | 3 | (9) | 1 | (5) | 1 | (25) | 2 | (25) | 7 | (44) |
Granulomatous disease | 0 | (0) | 1 | (5) | 2 | (50) | 4 | (50) | 2 | (13) |
Villous atrophy | 0 | (0) | 2 | (11) | 0 | (0) | 0 | (0) | 3 | (19) |
Chronic inflammatory intestinal disease | 0 | (0) | 2 | (11) | 1 | (25) | 1 | (13) | 0 | (0) |